Malformation of urachus

This code signifies a congenital anomaly of the urachus, a fibrous remnant of the allantois that connects the fetal bladder to the umbilicus. Malformations can include a patent urachus (remaining open), urachal cyst (fluid-filled sac), urachal sinus (opening to the umbilicus), or urachal diverticulum (outpouching of the bladder). These conditions represent incomplete obliteration of the urachus after birth.

Use this code for patients diagnosed with any congenital malformation of the urachus, such as a patent urachus, urachal cyst, urachal sinus, or urachal diverticulum. Documentation supporting this code includes imaging studies (e.g., ultrasound, CT, MRI) confirming the anomaly, surgical reports detailing repair, or clinical notes describing the presence of such a malformation.

• Differentiate between congenital and acquired conditions; this code is specifically for congenital malformations.
• Ensure documentation clearly specifies the type of urachal malformation (e.g., patent, cyst, sinus) to support the diagnosis.
• Consider sequencing this code as a primary diagnosis if the urachal malformation is the reason for the encounter, or as a secondary diagnosis if it's an incidental finding or contributing factor to another condition.