Arthrogryposis multiplex congenita

This code represents a rare congenital disorder characterized by multiple joint contractures present at birth, affecting two or more body areas. These contractures result from decreased fetal movement in utero, leading to fibrous or bony ankylosis of the joints. The condition can range from mild involvement to severe, widespread contractures impacting mobility and development.

Assign this code for patients diagnosed with arthrogryposis multiplex congenita, regardless of the specific underlying etiology. Documentation should clearly state the diagnosis of AMC, often noting the presence of multiple fixed joint contractures identified at birth or shortly thereafter. This code is appropriate for initial diagnosis and subsequent encounters related to the management of this condition.

• Do not confuse with isolated congenital contractures of a single joint; AMC requires involvement of multiple joints in different body areas.
• Code any associated congenital anomalies or underlying conditions (e.g., neurological disorders, muscular dystrophies) separately.
• Ensure documentation specifies "congenital" to differentiate from acquired contractures.