Pansynostosis

Pansynostosis refers to the premature fusion of all cranial sutures, leading to a uniformly small and abnormally shaped skull. This condition severely restricts brain growth, often resulting in significant neurological impairment and increased intracranial pressure. It is a rare and severe form of craniosynostosis.

This code is used when documentation explicitly states "pansynostosis" or describes the premature fusion of all major cranial sutures. It applies to cases where imaging studies (e.g., CT scans) confirm the complete closure of the sagittal, coronal, lambdoid, and metopic sutures. Use this code for congenital cases identified at birth or early infancy.

• Ensure documentation specifies "pansynostosis" rather than a single or multiple specific suture fusions.
• Do not use this code for isolated or partial craniosynostosis; specific codes exist for those conditions.
• Code any associated congenital anomalies or neurological complications separately.