Other multi-suture craniosynostosis

This code represents a congenital condition characterized by the premature fusion of multiple cranial sutures, excluding bilateral coronal or bilateral lambdoid sutures. This premature fusion restricts normal skull growth, potentially leading to abnormal head shape and increased intracranial pressure. It encompasses various patterns of multi-suture synostosis not specifically classified elsewhere.

Use this code when documentation indicates craniosynostosis involving more than one cranial suture, and the specific pattern does not fall under bilateral coronal or bilateral lambdoid synostosis. This diagnosis is typically made based on physical examination, imaging studies (e.g., CT scan), and genetic evaluation. It applies to cases such as bicoronal and metopic synostosis, or complex synostosis involving three or more sutures.

• Ensure the documentation clearly specifies the involvement of multiple sutures and explicitly rules out bilateral coronal or bilateral lambdoid synostosis.
• Do not use this code if the craniosynostosis is limited to a single suture or if it is specifically bilateral coronal (Q75.022) or bilateral lambdoid (Q75.042).
• Review imaging reports and operative notes for precise identification of fused sutures to select the most specific code available.