Prune belly syndrome

This code represents Prune Belly Syndrome, also known as Eagle-Barrett syndrome, a rare congenital disorder characterized by a triad of symptoms: deficient abdominal wall musculature, undescended testes (cryptorchidism) in males, and urinary tract abnormalities, including hydronephrosis and megaureters. The lax abdominal wall gives a wrinkled, prune-like appearance.

Use this code when documentation explicitly states a diagnosis of Prune Belly Syndrome. This diagnosis is typically made prenatally via ultrasound or at birth based on the characteristic physical findings and confirmed by imaging studies of the urinary tract.

• Ensure documentation clearly specifies "Prune Belly Syndrome" and not just individual components like cryptorchidism or hydronephrosis.
• Code all associated congenital anomalies separately, such as specific urinary tract malformations (e.g., congenital hydronephrosis, megaureter) and cryptorchidism.
• Consider sequencing this code as the primary diagnosis when it is the main reason for the encounter, especially for initial evaluations or management of the syndrome itself.