Congenital absence of breast with absent nipple

This code describes a rare congenital anomaly characterized by the complete absence of breast tissue and the corresponding nipple structure. It represents a severe form of amastia, where both the mammary gland and its associated areolar-nipple complex fail to develop during embryogenesis.

Assign this code for patients diagnosed with a complete lack of breast and nipple formation from birth. Documentation should clearly state the congenital nature of the absence and specify that both the breast and nipple are missing, often noted during initial physical examination or imaging studies.

• Differentiate from acquired absence of breast (e.g., post-mastectomy) or other congenital breast anomalies where some tissue or nipple may be present.
• Ensure documentation explicitly states "absent nipple" in addition to "absent breast" to support this specific code.
• Consider laterality (e.g., unilateral vs. bilateral) if specified in the clinical record, though this code does not differentiate laterality.