Congenital leukonychia

This code represents a congenital anomaly characterized by the presence of white discoloration or spots on the nails from birth. It is a developmental defect affecting the nail matrix, resulting in abnormal keratinization. The condition is typically benign and cosmetic.

Assign this code when documentation specifies leukonychia present at birth, indicating a congenital origin. This diagnosis is supported by physician notes detailing the onset of nail discoloration since birth or early infancy, distinguishing it from acquired forms.

• Differentiate from acquired leukonychia, which would be coded to a symptom code (e.g., R68.89 for other general symptoms).
• Ensure documentation explicitly states "congenital" or "present at birth" to support this specific code.
• This code is typically a primary diagnosis unless another more severe congenital anomaly is being treated concurrently.