Acute idiopathic pulmonary hemorrhage in infants

This code signifies sudden, unexplained bleeding into the lungs of an infant, not attributable to a known cause like trauma or a bleeding disorder. It presents as respiratory distress, hemoptysis, or blood-tinged secretions in an otherwise healthy infant.

Assign this code when documentation clearly states "acute idiopathic pulmonary hemorrhage" in an infant, typically under one year of age, and investigations have ruled out other causes. Supporting documentation should include clinical findings of pulmonary bleeding and negative workup for coagulopathies or other specific etiologies.

• Ensure the patient's age is documented as an infant; otherwise, consider other pulmonary hemorrhage codes.
• Differentiate from perinatal pulmonary hemorrhage (P26.-) which occurs during the perinatal period (birth up to 28 days).
• Confirm that von Willebrand disease (D68.0-) has been ruled out, as it is an Excludes1 condition.