Pure hyperglyceridemia

This code represents a primary lipid disorder characterized by significantly elevated levels of triglycerides in the blood, with normal or near-normal cholesterol levels. It is a form of hyperlipidemia where the primary abnormality is an excess of very low-density lipoproteins (VLDL) due to impaired clearance or overproduction.

Use this code when diagnostic testing confirms isolated hypertriglyceridemia, typically with triglyceride levels exceeding 200 mg/dL (or 2.26 mmol/L) and total cholesterol and LDL cholesterol within normal limits. Documentation should clearly state "pure hyperglyceridemia" or "isolated hypertriglyceridemia" as the primary diagnosis.

• Differentiate from mixed hyperlipidemia (elevated cholesterol and triglycerides) or other specific dyslipidemias.
• Ensure documentation specifies "pure" or "isolated" to avoid confusion with broader hyperlipidemia codes.
• Consider sequencing if other metabolic conditions, such as diabetes, are also present and contributing to the hypertriglyceridemia.