Congenital factor IX disorder

This code represents a hereditary bleeding disorder characterized by a deficiency in coagulation factor IX, also known as hemophilia B or Christmas disease. It results in impaired blood clotting, leading to prolonged bleeding episodes following injury, surgery, or spontaneously.

Apply this code when documentation confirms a congenital deficiency of factor IX, typically diagnosed through coagulation factor assays. This code is appropriate for patients with a lifelong history of this specific clotting factor defect.

• Differentiate from acquired factor IX deficiency, which would be coded differently.
• Always sequence this code as a primary diagnosis when it is the reason for the encounter, or as a secondary diagnosis when it impacts treatment of another condition.
• Ensure documentation specifies "congenital" or "hereditary" to support the use of this specific code.