Rheumatic fever without mention of heart involvement

This code signifies an acute inflammatory disease that can develop as a complication of untreated or inadequately treated streptococcal infection, specifically affecting tissues other than the heart. It represents the systemic manifestations of rheumatic fever, such as arthritis or chorea, without any documented cardiac involvement.

Use this code when the medical record clearly documents a diagnosis of rheumatic fever, and there is no mention or evidence of carditis, valvular disease, or other cardiac complications. This typically applies to initial episodes or follow-up care where only extracardiac manifestations are present.

• Do not use this code if any form of rheumatic heart disease (e.g., carditis, valvulitis) is documented; instead, select a more specific code from categories 391-392.
• Ensure documentation explicitly states "without heart involvement" or describes only non-cardiac manifestations.
• Sequence this code as the primary diagnosis when rheumatic fever without heart involvement is the reason for the encounter.