Other acute rheumatic heart disease

This code signifies acute inflammatory conditions affecting the heart valves, myocardium, or pericardium, stemming from a recent rheumatic fever episode, that are not specifically classified elsewhere. It indicates active rheumatic carditis with manifestations beyond isolated valve involvement.

Apply this code when documentation specifies acute rheumatic heart disease with cardiac involvement that is not solely valvular, or when the specific valve(s) affected are not clearly identified. This code is appropriate when the acute phase of rheumatic fever is impacting the heart in a generalized or unspecified manner.

• Ensure documentation explicitly states "acute" rheumatic heart disease and indicates cardiac involvement.
• Do not use if a specific acute rheumatic valvulitis (e.g., mitral, aortic) is clearly documented; use the more specific code.
• Always sequence this code after the acute rheumatic fever code (e.g., 390) if the fever is still active.