Rheumatic diseases of pulmonary valve

This code signifies inflammatory conditions affecting the pulmonary valve due to rheumatic fever. It encompasses both acute and chronic manifestations of rheumatic heart disease specifically impacting the pulmonary valve, leading to dysfunction such as stenosis or insufficiency.

Use this code when documentation explicitly states rheumatic involvement of the pulmonary valve, whether active or a sequela of past rheumatic fever. This diagnosis is supported by findings of pulmonary valve stenosis, regurgitation, or other structural changes attributed to rheumatic disease, often confirmed by echocardiography.

• Differentiate from non-rheumatic pulmonary valve disorders; documentation must specify rheumatic etiology.
• Code any associated heart failure or other cardiac complications separately.
• Ensure the medical record clearly links the pulmonary valve disease to a history or current diagnosis of rheumatic fever.