Other chronic pulmonary heart diseases

This code represents chronic heart conditions primarily affecting the right side of the heart, caused by long-standing diseases of the lungs or pulmonary vasculature. It signifies a sustained increase in pulmonary artery pressure leading to right ventricular hypertrophy and/or dilation, excluding acute forms of pulmonary heart disease.

Use this code for patients with established cor pulmonale due to chronic lung conditions such as severe COPD, interstitial lung disease, or chronic pulmonary embolism. Documentation should clearly indicate a chronic nature of the pulmonary hypertension and its impact on the right ventricle, often evidenced by echocardiogram findings or right heart catheterization.

• Do not use for acute cor pulmonale; refer to codes for acute pulmonary heart disease.
• Always code the underlying chronic lung disease first, as it is the etiology of the pulmonary heart disease.
• Ensure documentation specifies "chronic" to differentiate from acute or unspecified pulmonary heart disease.