Arteriovenous fistula of pulmonary vessels

This code describes an abnormal, direct connection between an artery and a vein within the pulmonary circulation, bypassing the capillary bed. This shunting of blood can lead to hypoxemia and other cardiopulmonary complications.

Apply this code when documentation confirms the presence of a congenital or acquired arteriovenous malformation or fistula specifically affecting the pulmonary arteries and veins. Supporting documentation would include imaging reports (e.g., CT angiography, pulmonary angiography) or surgical findings.

• Differentiate from systemic arteriovenous fistulas, which are coded elsewhere.
• Consider additional codes for associated symptoms or complications, such as hypoxemia or heart failure.
• Ensure documentation clearly specifies the pulmonary location of the fistula.