Polyarteritis nodosa

This code represents a rare, severe systemic necrotizing vasculitis affecting medium-sized arteries, leading to inflammation and damage in various organ systems. It is characterized by widespread inflammation of the arterial walls, often resulting in aneurysms, thrombosis, and infarction of affected tissues.

Use this code for patients diagnosed with classic polyarteritis nodosa, confirmed by biopsy showing necrotizing inflammation of medium-sized arteries. Documentation should clearly indicate the diagnosis of polyarteritis nodosa, often supported by clinical presentation, imaging findings, and laboratory results.

• Ensure documentation specifies "polyarteritis nodosa" to differentiate from other forms of vasculitis.
• Code associated organ manifestations (e.g., renal failure, neuropathy) separately as secondary diagnoses.
• This code is for the active disease; consider appropriate remission codes if applicable for other vasculitides, though less common for classic PAN.