Congenital reduction deformities of brain

This code signifies a birth defect characterized by an incomplete development or absence of brain tissue. It encompasses a range of conditions where the brain is abnormally small or has structural deficiencies present at birth. These deformities can lead to varying degrees of neurological impairment.

Apply this code when documentation clearly indicates a congenital malformation resulting in reduced brain mass or significant structural abnormalities of the brain. This includes conditions like microcephaly, anencephaly, or other severe cerebral hypoplasia diagnosed at birth or in early infancy. Supporting documentation should specify the congenital nature and the specific type of brain reduction deformity.

• Differentiate from acquired brain atrophy or damage, which would be coded elsewhere.
• Ensure the documentation explicitly states "congenital" or "at birth" to support this code.
• Consider additional codes for associated neurological deficits or syndromes, if documented.