Congenital mitral insufficiency

This code represents a congenital heart defect where the mitral valve, located between the left atrium and left ventricle, fails to close properly from birth. This improper closure leads to regurgitation of blood back into the left atrium during ventricular systole, causing volume overload and potential cardiac dysfunction.

Use this code for documented cases of mitral valve insufficiency that are present at birth, often identified during infancy or early childhood. Documentation should clearly state "congenital mitral insufficiency" or "congenital mitral regurgitation," supported by echocardiogram findings or other diagnostic studies confirming the structural anomaly.

• Differentiate from acquired mitral insufficiency (e.g., rheumatic, ischemic), which would be coded differently.
• Always review documentation for laterality if specified, though mitral valve is a single structure.
• Consider sequencing with other congenital cardiac anomalies if present, as this condition often co-occurs.