Renal agenesis and dysgenesis

This code represents congenital conditions where one or both kidneys are absent (agenesis) or abnormally developed (dysgenesis). These are severe birth defects affecting the urinary system, often leading to significant renal impairment or failure.

Use this code for documented cases of a newborn or fetus diagnosed with renal agenesis (unilateral or bilateral) or renal dysgenesis. Supporting documentation includes imaging studies (e.g., ultrasound, MRI) confirming the absence or malformation of kidney tissue, and clinical notes detailing the diagnosis.

• Differentiate from other congenital anomalies of the kidney and ureter (CAKUT) that involve structural abnormalities but not complete absence or severe malformation of the kidney itself.
• Consider sequencing this code as the primary diagnosis when it is the main reason for the encounter or hospitalization.
• Look for specific documentation of "agenesis" or "dysgenesis" of the kidney; "hypoplasia" or "aplasia" may also be used interchangeably with dysgenesis or agenesis, respectively.