Brazilian purpuric fever

This code identifies a rare and severe bacterial infection, specifically Haemophilus influenzae biogroup aegyptius, characterized by acute onset of fever, purpuric rash, and often leading to septic shock and high mortality, particularly in young children. It is a systemic illness with a distinct clinical presentation.

Assign this code when documentation clearly indicates a diagnosis of Brazilian purpuric fever, typically following a preceding conjunctivitis. This diagnosis is usually made based on clinical presentation in endemic areas and confirmed by microbiological testing. Supporting documentation should detail the characteristic purpuric rash, fever, and evidence of systemic infection.

• Ensure the documentation explicitly states "Brazilian purpuric fever" or provides a definitive diagnosis of Haemophilus influenzae biogroup aegyptius infection with the characteristic clinical syndrome.
• Do not confuse this with other forms of purpura or septicemia without the specific etiology and clinical picture of Brazilian purpuric fever.
• Consider sequencing this code as the primary diagnosis when it is the reason for the encounter, followed by codes for any associated complications like septic shock or organ failure.