Mycosis fungoides, spleen

This diagnosis code signifies Mycosis Fungoides, a rare, slow-growing cutaneous T-cell lymphoma, specifically when it has metastasized to or originated in the spleen. It indicates systemic involvement of this primary skin lymphoma beyond the integumentary system.

Use this code when documentation confirms a diagnosis of Mycosis Fungoides with evidence of splenic involvement, typically identified through imaging (e.g., CT, MRI, PET scan) or biopsy. Supporting documentation should clearly state "Mycosis Fungoides with splenic involvement" or similar.

• Always confirm the specific site of involvement; Mycosis Fungoides can affect various organs.
• Sequence this code after the primary diagnosis of Mycosis Fungoides if the splenic involvement is a manifestation of the primary disease.
• Distinguish from other non-Hodgkin lymphomas affecting the spleen, ensuring the primary diagnosis is Mycosis Fungoides.