Mycosis fungoides, lymph nodes of multiple sites

This code signifies a rare, slow-growing cutaneous T-cell lymphoma, specifically Mycosis Fungoides, that has spread to involve lymph nodes in more than one distinct anatomical region. It indicates systemic involvement beyond the skin, representing a more advanced stage of the disease.

Use this code when documentation clearly states a diagnosis of Mycosis Fungoides with confirmed involvement of multiple lymph node sites. This typically follows biopsy and pathological confirmation of lymphoma cells within the lymph nodes.

• Ensure documentation specifies "multiple sites" for lymph node involvement; otherwise, a more specific site code may be appropriate.
• Do not confuse with codes for Mycosis Fungoides limited to the skin or involving only a single lymph node region.
• Always sequence this code after any underlying cause or primary malignancy if applicable, though Mycosis Fungoides is often considered the primary diagnosis itself.