Sezary disease, lymph nodes of head, face, and neck

This code signifies Sezary disease, a rare and aggressive form of cutaneous T-cell lymphoma, specifically when it involves the lymph nodes located in the head, face, and neck regions. It is characterized by the presence of Sezary cells (malignant T-lymphocytes) in the skin, blood, and lymph nodes.

Apply this code when documentation clearly indicates a diagnosis of Sezary disease with confirmed involvement of lymph nodes in the head, face, or neck. This typically requires pathology reports confirming Sezary cells within these specific lymph node sites.

• Ensure the documentation explicitly states "Sezary disease" and specifies lymph node involvement in the head, face, or neck.
• Do not use this code for other types of cutaneous T-cell lymphoma or for Sezary disease without confirmed lymph node involvement in these specific areas.
• Sequence this code as a primary diagnosis when it is the reason for the encounter, or as a secondary diagnosis if the encounter is for a complication or treatment related to the Sezary disease.