Sezary disease, intra-abdominal lymph nodes

This code signifies a rare, aggressive form of cutaneous T-cell lymphoma (CTCL) known as Sézary syndrome, specifically when the disease has spread to involve the lymph nodes located within the abdominal cavity. It indicates systemic involvement beyond the skin, impacting internal lymphatic structures.

Apply this code when documentation explicitly states a diagnosis of Sézary disease with confirmed involvement of intra-abdominal lymph nodes. This typically follows imaging studies (e.g., CT, MRI) or biopsy results demonstrating malignant Sézary cells in these specific nodal sites.

• Ensure documentation clearly specifies "intra-abdominal" lymph node involvement, not just general lymphadenopathy.
• Do not confuse with other types of CTCL or lymphomas affecting different lymph node regions.
• Sequence as a primary diagnosis when it is the reason for the encounter, or as a secondary diagnosis if managing complications or other primary conditions.