Sezary disease, nodes of inguinal region and lower limb

This code signifies Sezary disease, a rare and aggressive form of cutaneous T-cell lymphoma, specifically when it affects the lymph nodes located in the inguinal region and/or the lower limbs. It indicates systemic involvement of the disease beyond the skin.

Use this code when diagnostic imaging (e.g., CT, MRI, PET scan) or biopsy confirms Sezary disease with documented involvement of lymph nodes in the groin or leg. Documentation should explicitly state the presence of malignant cells in these specific lymph node areas.

• Ensure documentation clearly specifies "Sezary disease" and not another type of cutaneous T-cell lymphoma.
• Verify the exact anatomical location of lymph node involvement; this code is specific to inguinal and lower limb nodes.
• Sequence this code as a primary diagnosis when the lymph node involvement is the focus of the encounter, or as a secondary diagnosis when treating the systemic manifestation of Sezary disease.