Anaplastic large cell lymphoma, ALK-pos, intrapelv nodes

This code signifies a rare and aggressive type of non-Hodgkin lymphoma characterized by the presence of anaplastic large cells and a positive anaplastic lymphoma kinase (ALK) protein. Specifically, it indicates that this malignancy is located within the lymph nodes of the pelvic region.

Use this code when documentation confirms a diagnosis of anaplastic large cell lymphoma that is ALK-positive, with the primary site of involvement being the intrapelvic lymph nodes. This typically follows biopsy and immunohistochemical staining confirming ALK positivity, along with imaging studies or surgical findings localizing the disease to the pelvis.

• Ensure documentation explicitly states "ALK-positive" for anaplastic large cell lymphoma; otherwise, a different code for ALK-negative or unspecified ALK status should be used.
• Verify the specific anatomical site of involvement; this code is only for intrapelvic lymph nodes.
• Consider sequencing this code as the primary diagnosis when it is the reason for the encounter, followed by any associated symptoms or complications.