Anaplastic large cell lymphoma, ALK-neg, intra-abd nodes

This code signifies a rare and aggressive type of non-Hodgkin lymphoma, specifically anaplastic large cell lymphoma (ALCL), which tests negative for the anaplastic lymphoma kinase (ALK) protein. The disease is located within the lymph nodes inside the abdominal cavity. This diagnosis indicates a specific subtype of ALCL with distinct biological and clinical characteristics.

Use this code when documentation confirms a diagnosis of ALK-negative anaplastic large cell lymphoma, and imaging or biopsy reports specify involvement of intra-abdominal lymph nodes. This code is appropriate for initial diagnosis, staging, and subsequent encounters where the primary site of disease remains intra-abdominal. Ensure the pathology report explicitly states "ALK-negative."

• Confirm the ALK status (negative) is clearly documented by pathology.
• Verify the anatomical site of involvement is specifically "intra-abdominal lymph nodes" and not other nodal or extranodal sites.
• Do not confuse with ALK-positive ALCL or other subtypes of non-Hodgkin lymphoma.