Anaplstc lg cell lymph, ALK-neg, nodes of ing rgn & low lmb

This code signifies a rare and aggressive type of non-Hodgkin lymphoma, specifically anaplastic large cell lymphoma (ALCL), which tests negative for the anaplastic lymphoma kinase (ALK) protein. The diagnosis is further localized to the lymph nodes situated in the inguinal region and the lower limb.

Apply this code when documentation confirms a pathological diagnosis of ALK-negative ALCL affecting the lymph nodes of the groin or leg. This typically follows a biopsy and immunohistochemical staining demonstrating ALK negativity. Use this code for primary diagnoses or when this specific lymphoma is the focus of treatment.

• Ensure documentation explicitly states "ALK-negative" for ALCL; otherwise, a different ALCL code may be appropriate.
• Verify the anatomical site is precisely the inguinal region or lower limb lymph nodes.
• Do not confuse with ALK-positive ALCL or other specified/unspecified ALCL types.