Anaplastic large cell lymphoma, ALK-neg, intrapelv nodes

This diagnosis code specifies a rare and aggressive form of non-Hodgkin lymphoma characterized by the absence of the anaplastic lymphoma kinase (ALK) gene rearrangement, affecting lymph nodes located within the pelvic region. ALK-negative anaplastic large cell lymphoma (ALCL) generally has a less favorable prognosis than its ALK-positive counterpart.

Use this code when documentation confirms a pathological diagnosis of ALK-negative anaplastic large cell lymphoma. The specific involvement of intrapelvic lymph nodes must be clearly stated in the pathology report or imaging findings. This code is appropriate for initial diagnosis, staging, and follow-up care where the primary site of involvement is identified as intrapelvic lymph nodes.

• Ensure the pathology report explicitly states "ALK-negative" to differentiate from ALK-positive ALCL.
• Verify the anatomical location of the involved lymph nodes is specifically "intrapelvic" to avoid miscoding other lymph node sites.
• Sequence this code as the primary diagnosis when it is the reason for the encounter, followed by any associated symptoms or complications.