Mature T/NK-cell lymphomas, unspecified, spleen

This code signifies a malignant proliferation of mature T-lymphocytes or natural killer (NK) cells, where the specific subtype of lymphoma is not identified, and the primary or most significant site of involvement is the spleen. These are aggressive lymphomas originating from the immune system.

Utilize this code when documentation confirms a diagnosis of mature T-cell or NK-cell lymphoma, but the pathologist or clinician has not specified a more precise subtype (e.g., peripheral T-cell lymphoma, not otherwise specified). The medical record must explicitly indicate splenic involvement as the primary or significant site.

• Only assign this code when a more specific mature T/NK-cell lymphoma code is unavailable.
• Ensure documentation clearly states "unspecified" or "not otherwise specified" regarding the lymphoma subtype.
• Verify the spleen is documented as the primary or significant site of involvement.