Primary cutaneous CD30-positive T-cell prolif not remission

This code represents a group of rare, non-Hodgkin lymphomas characterized by the proliferation of CD30-positive T-cells primarily affecting the skin. These cutaneous lymphomas include conditions such as primary cutaneous anaplastic large cell lymphoma (pcALCL) and lymphomatoid papulosis (LyP) that have not yet achieved a state of remission.

Use this code when documentation confirms a diagnosis of a primary cutaneous CD30-positive T-cell proliferation that is still active or persistent, rather than in remission. This applies to initial diagnoses, relapses, or ongoing disease where remission has not been achieved. Supporting documentation should clearly state the CD30 positivity and the cutaneous nature of the T-cell proliferation.

• Differentiate from systemic CD30-positive T-cell lymphomas, which would be coded elsewhere.
• Ensure documentation specifies "primary cutaneous" to avoid confusion with secondary skin involvement.
• Do not use if the patient has achieved complete remission; instead, consider codes for personal history of malignancy.