Prolymphocytic leukemia of T-cell type, in remission

This code signifies a malignant neoplasm of the hematopoietic system characterized by the proliferation of mature T-lymphocytes with prolymphocytic morphology, which is currently in a state of remission. It indicates that the patient has previously been diagnosed with T-cell prolymphocytic leukemia and, following treatment, shows no evidence of active disease.

Use this code when documentation explicitly states a diagnosis of T-cell prolymphocytic leukemia and confirms that the disease is currently in remission. This typically follows successful chemotherapy, immunotherapy, or stem cell transplantation. Supporting documentation should include pathology reports confirming T-cell lineage and physician notes indicating remission status.

• Always ensure documentation specifies "T-cell type" and "in remission" to accurately assign this code.
• Do not confuse this with active disease codes (C91.60) or B-cell prolymphocytic leukemia.
• Sequence this code as a primary diagnosis when the encounter is for management of the remission status or surveillance.