Von Willebrand disease, unspecified

This code signifies a diagnosis of Von Willebrand disease (VWD) where the specific type of VWD has not been determined or documented. VWD is a hereditary bleeding disorder caused by a deficiency or dysfunction of von Willebrand factor, a protein essential for normal blood clotting. Patients typically present with mucocutaneous bleeding symptoms.

Use this code when the medical record clearly states a diagnosis of Von Willebrand disease but does not specify the type (e.g., Type 1, Type 2, Type 3). This code is appropriate when initial diagnostic workup is underway or when the specific type remains undiagnosed after evaluation. Documentation should indicate VWD without further subtyping.

• Avoid using this code if a specific type of Von Willebrand disease (e.g., D68.01 for Type 1) is documented.
• Query the provider for clarification on the specific type of VWD if possible, to allow for more precise coding.
• This code should be sequenced as the primary diagnosis when VWD is the reason for the encounter.