Von Willebrand disease, type 1

This code represents Von Willebrand disease (VWD) type 1, a mild to moderate inherited bleeding disorder characterized by a quantitative defect in von Willebrand factor (VWF). Patients typically have reduced levels of functionally normal VWF, leading to impaired platelet adhesion and aggregation, and sometimes reduced factor VIII levels.

Use this code when documentation explicitly states a diagnosis of Von Willebrand disease, type 1, often confirmed by laboratory testing showing reduced VWF antigen and activity levels. This diagnosis is typically made after evaluation for symptoms like easy bruising, prolonged bleeding from cuts, nosebleeds, or heavy menstrual bleeding.

• Ensure the physician's documentation specifies "type 1" VWD; do not assume the type.
• Distinguish from other types of VWD (e.g., type 2 or 3), which have different code assignments.
• Code any associated bleeding manifestations or complications separately, if applicable.