Meconium ileus in cystic fibrosis

This code identifies a specific type of intestinal obstruction occurring in neonates, where the meconium (first stool) is abnormally thick and sticky, leading to a blockage in the small intestine. This condition is a hallmark gastrointestinal manifestation of cystic fibrosis.

Use this code when documentation explicitly states meconium ileus and confirms a diagnosis of cystic fibrosis in the patient. This is typically seen in neonates or infants presenting with abdominal distension, vomiting, and failure to pass meconium.

• Always confirm the causal link between meconium ileus and cystic fibrosis in the documentation.
• Do not use this code if cystic fibrosis is not documented as the underlying cause; refer to the Excludes1 note.
• Code any associated complications of the meconium ileus (e.g., perforation, volvulus) separately.