Cystic fibrosis with other intestinal manifestations

This code signifies cystic fibrosis (CF) where the patient exhibits intestinal complications other than meconium ileus. These manifestations can include distal intestinal obstruction syndrome (DIOS), intussusception, rectal prolapse, or other gastrointestinal issues directly attributable to CF.

Apply this code when documentation clearly indicates a diagnosis of cystic fibrosis alongside specific intestinal complications that are not meconium ileus. This is appropriate for patients experiencing recurrent DIOS, chronic constipation refractory to standard treatment in CF, or other documented intestinal pathology linked to their CF.

• Ensure the medical record specifies an intestinal manifestation other than meconium ileus.
• Do not use this code if the only intestinal manifestation is meconium ileus; a different subcategory of E84.1 would be more appropriate.
• Code any specific intestinal complications (e.g., K56.5 for DIOS) as secondary diagnoses, following the primary CF code.