Progressive supranuclear ophthalmoplegia

This code identifies a rare, progressive neurodegenerative disorder characterized by the degeneration of neurons in the brainstem and basal ganglia. Key features include ophthalmoplegia (impaired eye movements, particularly vertical gaze), postural instability leading to falls, and cognitive decline. It is also known as Steele-Richardson-Olszewski syndrome.

Assign this code for patients diagnosed with progressive supranuclear palsy (PSP) based on clinical presentation and neurological examination findings. Documentation should clearly indicate the presence of the characteristic symptoms, such as vertical gaze palsy, unexplained falls, and cognitive changes, consistent with a neurologist's diagnosis of PSP.

• Differentiate from Parkinson's disease (G20) or multiple system atrophy (G90.3) which can have overlapping symptoms but distinct diagnostic criteria.
• Ensure documentation specifies "progressive supranuclear ophthalmoplegia" or "Steele-Richardson-Olszewski syndrome" for accurate code assignment.
• Code any associated symptoms or complications, such as dysphagia (R13.1x) or dementia (F02.80, F02.81), as secondary diagnoses.