Other degenerative diseases of the basal ganglia

This code signifies a group of neurological disorders characterized by the progressive degeneration of neurons within the basal ganglia, leading to a variety of motor and cognitive impairments. These conditions are distinct from more common basal ganglia diseases like Parkinson's disease or Huntington's chorea, representing less frequently encountered or atypical presentations.

Assign this code when documentation specifies a degenerative basal ganglia disorder that does not fit into more specific ICD-9-CM categories. This includes conditions like progressive supranuclear palsy (PSP), corticobasal degeneration (CBD), or multiple system atrophy (MSA) when a more precise code is unavailable or the diagnosis is stated generally as "other degenerative basal ganglia disease." Supporting documentation should clearly indicate a degenerative process affecting the basal ganglia.

• Do not use this code if a more specific ICD-9-CM code exists for the documented basal ganglia disorder.
• Ensure the physician's documentation explicitly states "degenerative" and "basal ganglia" or a specific condition falling under this umbrella.
• Consider sequencing this code as a primary diagnosis if it is the main reason for the encounter or admission.