Hereditary motor and sensory neuropathy

This code identifies a group of inherited neurological disorders characterized by progressive degeneration of peripheral nerves, leading to muscle weakness and sensory loss. It encompasses various forms of Charcot-Marie-Tooth (CMT) disease, which primarily affect motor and sensory neurons. The condition typically presents with distal muscle atrophy, foot deformities, and impaired sensation.

Assign this code when documentation explicitly states a diagnosis of hereditary motor and sensory neuropathy, including specific types of CMT disease (e.g., CMT1, CMT2, CMTX) without further specification of the exact genetic mutation. This code is appropriate for initial diagnosis and subsequent encounters for ongoing management of the condition. Supporting documentation should include neurological exam findings, nerve conduction studies, and genetic testing results if available.

• Do not use this code if a more specific genetic subtype of hereditary neuropathy is documented (e.g., G60.1 for Refsum's disease).
• Consider sequencing this code as a primary diagnosis when it is the reason for the encounter, or as a secondary diagnosis when managing complications or related conditions.
• Ensure documentation clearly distinguishes hereditary forms from acquired neuropathies to avoid miscoding.