Hereditary sensory neuropathy

This code signifies a group of inherited neurological disorders characterized by progressive degeneration of sensory neurons, primarily affecting the peripheral nervous system. Patients typically experience loss of sensation, particularly pain and temperature, leading to recurrent injuries, ulcers, and deformities, especially in the extremities.

Apply this code when documentation explicitly states a diagnosis of hereditary sensory neuropathy, often identified by specific types such as Hereditary Sensory and Autonomic Neuropathy (HSAN). This diagnosis is usually confirmed through genetic testing, nerve conduction studies, and clinical presentation of sensory deficits without significant motor involvement.

• Differentiate from other neuropathies; ensure "hereditary" and "sensory" are clearly documented.
• Be aware that specific types of HSAN (e.g., HSAN type I, II, III) may have more granular ICD-10 codes, but for ICD-9-CM, this is the most appropriate general code.
• Consider sequencing this code as the primary diagnosis when it is the main reason for the encounter, especially for management of related complications.