Idiopathic progressive polyneuropathy

This code signifies a chronic, generalized disorder affecting multiple peripheral nerves, where the underlying cause is unknown. It is characterized by progressive weakness, sensory loss, and sometimes autonomic dysfunction, without an identifiable etiology such as diabetes, toxins, or autoimmune disease.

Apply this code when documentation clearly states "idiopathic progressive polyneuropathy" or "chronic inflammatory demyelinating polyneuropathy (CIDP)" when the cause is not specified. It is appropriate for cases where extensive diagnostic workup has failed to identify a specific cause for the polyneuropathy.

• Ensure the physician's documentation explicitly states "idiopathic" or that all known causes have been ruled out.
• Do not use this code if a specific cause for the polyneuropathy (e.g., diabetic, toxic, paraneoplastic) is identified; instead, code the specific type.
• Consider sequencing this code as the primary diagnosis if it is the main reason for the encounter and treatment.