Celiac artery compression syndrome

This code represents Celiac Artery Compression Syndrome, also known as Dunbar syndrome or Median Arcuate Ligament Syndrome (MALS). It is a rare condition where the median arcuate ligament, a fibrous arch of the diaphragm, compresses the celiac artery and sometimes the celiac ganglion, leading to abdominal pain and other gastrointestinal symptoms.

Use this code when documentation clearly indicates a diagnosis of celiac artery compression syndrome. This diagnosis is typically supported by imaging studies (e.g., CT angiography, MRA, duplex ultrasound demonstrating celiac artery stenosis with post-stenotic dilation) and clinical symptoms such as postprandial abdominal pain, weight loss, and nausea.

• Ensure physician documentation explicitly states "celiac artery compression syndrome" or "median arcuate ligament syndrome."
• Do not confuse with other types of mesenteric ischemia or abdominal angina unless MALS is specifically diagnosed.
• Consider sequencing this code as the primary diagnosis when it is the reason for the encounter, especially for diagnostic workup or surgical intervention.