Subcorneal pustular dermatitis

This code identifies a rare, chronic inflammatory skin condition characterized by sterile pustules that form just beneath the stratum corneum. These pustules typically appear in an annular or serpiginous pattern, often on the trunk and proximal extremities, and may be accompanied by erythema and scaling. The condition is also known as Sneddon-Wilkinson disease.

Apply this code when documentation clearly indicates a diagnosis of subcorneal pustular dermatosis, Sneddon-Wilkinson disease, or a similar synonym. This diagnosis is typically made based on clinical presentation and confirmed by skin biopsy showing subcorneal pustule formation without evidence of infection.

• Differentiate from other pustular dermatoses, such as pustular psoriasis or impetigo, which have distinct ICD-10-CM codes.
• Ensure pathology reports confirm sterile pustules to support this diagnosis.
• Consider sequencing with codes for any associated systemic conditions, such as monoclonal gammopathy, if documented.