Subcorneal pustular dermatosis

This code represents subcorneal pustular dermatosis (SPD), also known as Sneddon-Wilkinson disease. It is a rare, chronic, benign inflammatory skin condition characterized by recurrent crops of sterile pustules that coalesce to form annular or serpiginous patterns, typically on the trunk and flexural areas. The pustules are superficial, located just beneath the stratum corneum, and often resolve with desquamation without scarring.

Use this code when documentation clearly indicates a diagnosis of subcorneal pustular dermatosis based on clinical presentation and often confirmed by skin biopsy showing subcorneal pustules with neutrophils. This diagnosis is typically made by a dermatologist. It applies to initial diagnoses as well as follow-up care for this chronic condition.

• Ensure the documentation specifies "subcorneal" to differentiate from other pustular dermatoses.
• Do not confuse with pustular psoriasis or other forms of pustular eruptions without clear pathological confirmation of SPD.
• Consider any associated systemic conditions, such as IgA monoclonal gammopathy, and code them separately if documented.