Lichen ruber moniliformis

This code describes a rare, chronic, and progressive variant of lichen planus characterized by linear or beaded papules and nodules, often arranged in a necklace-like pattern. The lesions typically affect the neck, axillae, and groin, and can be intensely pruritic. It represents a distinct morphological presentation within the broader spectrum of lichenoid dermatoses.

Use this code when documentation specifically identifies the patient's condition as lichen ruber moniliformis. This diagnosis is typically made based on characteristic clinical presentation and often confirmed by skin biopsy showing lichenoid inflammation with specific histopathological features. It should be applied when the physician's diagnosis clearly differentiates this rare form from other types of lichen planus.

• Ensure the physician's documentation explicitly states "lichen ruber moniliformis" to support this specific code.
• Do not confuse this with other forms of lichen planus (e.g., L43.0 for hypertrophic lichen planus) unless the documentation clearly indicates the moniliform variant.
• Consider additional codes for associated symptoms like pruritus (L29.x) if separately documented and treated.