Pityriasis rubra pilaris

This code represents pityriasis rubra pilaris, a rare, chronic inflammatory skin condition characterized by reddish-orange scaling plaques, often with islands of normal skin (nappes claires). It typically presents with follicular papules that coalesce into larger lesions, and can affect various body areas, including the scalp, trunk, and extremities.

Use this code when documentation clearly indicates a diagnosis of pityriasis rubra pilaris. This diagnosis is typically made by a dermatologist based on clinical presentation and sometimes confirmed by skin biopsy. It is appropriate for both initial diagnoses and subsequent encounters related to the management of this condition.

• Ensure the physician's documentation explicitly states "pityriasis rubra pilaris" to support this specific code.
• Do not confuse this with other forms of pityriasis, such as pityriasis rosea or pityriasis versicolor, which have distinct codes.
• Consider any associated manifestations or complications, such as erythroderma, and code them additionally if documented.