Pityriasis rubra pilaris

This code represents pityriasis rubra pilaris (PRP), a chronic inflammatory skin condition characterized by reddish-orange scaling plaques, often with islands of normal skin (nappes claires). It typically affects the scalp, face, trunk, and extremities, and can sometimes lead to erythroderma.

Use this code for documented cases of pityriasis rubra pilaris, confirmed by a dermatologist. This code is appropriate when the patient presents with the characteristic clinical features and a diagnosis has been established. Documentation should clearly state "pityriasis rubra pilaris."

• Differentiate from other generalized scaling dermatoses like psoriasis or eczema, which have distinct codes.
• Ensure the physician's documentation explicitly states "pityriasis rubra pilaris" to support code assignment.
• Consider any associated systemic manifestations or complications, though this code specifically addresses the skin condition.