Erythema elevatum diutinum

This code represents a rare, chronic, and persistent form of leukocytoclastic vasculitis characterized by symmetrical, firm, red-to-purple papules, plaques, and nodules, primarily affecting extensor surfaces of the extremities. Lesions are typically asymptomatic but can be tender or pruritic, and may ulcerate or scar.

Assign this code when documentation clearly indicates a diagnosis of erythema elevatum diutinum, often confirmed by skin biopsy showing leukocytoclastic vasculitis with prominent neutrophilic infiltration. This diagnosis is typically made by a dermatologist based on clinical presentation and histopathological findings.

• Ensure the physician's documentation explicitly states "erythema elevatum diutinum" to support this specific diagnosis.
• Do not confuse this with other forms of vasculitis or chronic inflammatory skin conditions without specific diagnostic confirmation.
• Consider co-reporting codes for any associated systemic conditions or underlying disorders, as this condition can be paraneoplastic or associated with infections or autoimmune diseases.