Other vasculitis limited to the skin

This code represents inflammatory conditions of the blood vessels that are exclusively confined to the skin, without systemic involvement. These vasculitides manifest as palpable purpura, petechiae, livedo reticularis, or ulcerations, resulting from immune complex deposition or direct vessel wall damage.

Use this code for diagnoses such as cutaneous leukocytoclastic vasculitis, urticarial vasculitis, or erythema elevatum diutinum when the physician explicitly documents that the vasculitis is limited to the skin. Documentation should clearly state the absence of internal organ involvement, such as kidney, lung, or gastrointestinal manifestations.

• Ensure documentation explicitly states "limited to the skin" or similar phrasing to differentiate from systemic vasculitides.
• Do not use this code if there is any evidence of systemic involvement; instead, code to the specific type of systemic vasculitis.
• Consider an additional code for the underlying cause if known and documented (e.g., drug-induced, infection-related).