Multifocal fibrosclerosis

This code represents a rare, systemic disorder characterized by the abnormal proliferation of fibrous tissue in multiple organs or sites throughout the body. It involves the hardening and thickening of tissues, which can impair organ function. The condition is often progressive and can affect various systems, including the retroperitoneum, mediastinum, and orbits.

Use this code when documentation explicitly states a diagnosis of multifocal fibrosclerosis. This diagnosis is typically made based on clinical presentation, imaging studies showing widespread fibrotic changes, and often confirmed by biopsy. It applies to cases where the fibrotic process is not localized to a single area but involves multiple distinct anatomical sites.

• Ensure the documentation clearly specifies "multifocal" involvement, not just a single site of fibrosclerosis.
• Distinguish from localized fibrosclerosis (e.g., retroperitoneal fibrosis without other systemic involvement) which would be coded differently.
• Code any associated organ dysfunction or complications separately, if documented, as secondary diagnoses.